buschke
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The coexistence of dermatofibrosis lenticularis disseminata, a hereditary connective tissue disorder characterised by the appearance of fibromatose papules (nevi) on the back and the extremities, and osteopoikilia, called osteodermatopoikilosis or Buschke- Ollendorff syndrome [6]. | La coexistencia de dermatofibrosis lenticularis disseminata, una alteración hereditaria del tejido conectivo caracterizada por la aparición de pápulas fibromatosas (nevos) en la espalda y las extremidades, y osteopoiquilia se denomina osteodermatopoiquilosis o síndrome de Buschke-Ollendorff6. |
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